The natural history of idiopathic pulmonary fibrosis (IPF) has been characterized as a
steady, predictable decline in lung function over time. Recent evidence suggests that some …

This Review provides an updated approach to the diagnosis of idiopathic pulmonary fibrosis
(IPF), based on a systematic search of the medical literature and the expert opinion of …

Context.—Malignant mesothelioma (MM) is an uncommon tumor that can be difficult to
diagnose. Objective.—To provide updated, practical guidelines for the pathologic diagnosis …

Background: In 2002 the American Thoracic Society/European Respiratory Society
(ATS/ERS) classification of idiopathic interstitial pneumonias (IIPs) defined seven specific …

This document is an international evidence-based guideline on the diagnosis and
management of idiopathic pulmonary fibrosis, and is a collaborative effort of the American …

In 50 of 94 patients with bronchiolitis obliterans we found no apparent cause or associated
disease, and the bronchiolitis obliterans occurred with patchy organizing pneumonia …

Despite the considerable progress in the classification of the idiopathic interstitial
pneumonias (IIPs), the lack of an international standard has resulted in variable and …

Background Lymphangioleiomyomatosis (LAM) is a progressive, cystic lung disease in
women; it is associated with inappropriate activation of mammalian target of rapamycin …

Idiopathic pulmonary fibrosis is an inexorably fatal disorder characterized by connective
tissue deposition within the terminal air spaces resulting in loss of lung function and …

Fibrosing alveolitis associated with systemic sclerosis (FASSc) has a better prognosis than
idiopathic pulmonary fibrosis. In view of recent reports that idiopathic nonspecific interstitial …