Acute exacerbation of idiopathic pulmonary fibrosis has been defined as an acute, clinically
significant, respiratory deterioration of unidentifiable cause. The objective of this …

Progressive fibrotic interstitial lung diseases (ILDs) are characterised by major reductions in
quality of life and survival and have similarities to certain malignancies. However, palliative …

Background: This guideline addresses the diagnosis of hypersensitivity pneumonitis (HP). It
represents a collaborative effort among the American Thoracic Society, Japanese …

Rationale: In interstitial lung disease complicating systemic sclerosis (SSc-ILD), the optimal
prognostic use of baseline pulmonary function tests (PFTs) and high-resolution computed …

Many patients with an idiopathic interstitial pneumonia (IIP) have clinical features that
suggest an underlying autoimmune process but do not meet established criteria for a …

Challenges for the effective management of interstitial lung diseases (ILDs) include
difficulties with the early detection of disease, accurate prognostication with baseline data …

Background At present, no approved pharmacotherapies are available for unclassifiable
interstitial lung disease (ILD), which is characterised by progressive fibrosis of the lung. We …

Background Transbronchial lung cryobiopsy (TBLC) is a novel technique for sampling lung
tissue for interstitial lung disease diagnosis. The aim of this study was to establish the …

Rationale: Pulmonary hypertension (PH) associated with fibrotic idiopathic interstitial
pneumonia (IIP; idiopathic pulmonary fibrosis and nonspecific interstitial pneumonia) …

In idiopathic interstitial pneumonia (IIP), the significance of connective tissue disease (CTD)
features in the absence of a specific CTD diagnosis remains unclear. We studied the clinical …