A proportion of people living with common variable immunodeficiency disorders develop
granulomatous-lymphocytic interstitial lung disease (GLILD). We aimed to develop a …

BACKGROUND An increased cancer risk in patients with sarcoidosis has been suggested,
although results are conflicting in a number of case-control and cohort studies. We …

Many patients with idiopathic pulmonary fibrosis (IPF) complain of chronic refractory cough.
Chronic cough is a distressing and disabling symptom with a major impact on quality of life …

Background: This guideline addresses the diagnosis of hypersensitivity pneumonitis (HP). It
represents a collaborative effort among the American Thoracic Society, Japanese …

The endothelins are a family of endothelium-derived peptides that possess a variety of
functions, including vasoconstriction. Endothelin-1 (ET-1) is up-regulated during tissue …

Pleuroparenchymal fibroelastosis (PPFE) is a rare condition characterised by predominantly
upper lobe pleural and subjacent parenchymal fibrosis, the latter being intra-alveolar with …

Background: Evidence-based guidelines are needed for effective delivery of home oxygen
therapy to appropriate patients with chronic obstructive pulmonary disease (COPD) and …

Within the spectrum of fibrosing interstitial lung diseases (ILDs) is a subset of patients who
have inexorable progression of pulmonary fibrosis despite treatment, which is known as the …

Objective To determine the prognostic value of pulmonary function test (PFT) trends at 1 and
2 years in interstitial lung disease (ILD) associated with systemic sclerosis (SSc). Methods …

Background and objective In patients with severe interstitial lung disease (ILD) progressing
despite conventional immunosuppression, rituximab, a B‐lymphocyte depleting monoclonal …