Steroid-responsive pulmonary hypertension in a patient with Langerhans' cell granulomatosis (histiocytosis X)

B Benyounes; B Crestani; A Couvelard; C Vissuzaine; M Aubier

doi:10.1378/chest.110.1.284

Steroid-responsive pulmonary hypertension in a patient with Langerhans' cell granulomatosis (histiocytosis X)

Chest. 1996 Jul;110(1):284-6. doi: 10.1378/chest.110.1.284.

Authors

B Benyounes¹, B Crestani, A Couvelard, C Vissuzaine, M Aubier

Affiliation

¹ Pulmonology Unit, Hŏpital Bichat, Paris, France.

PMID: 8681645
DOI: 10.1378/chest.110.1.284

Abstract

We report the case of a man with biopsy-proved pulmonary Langerhans' cell granulomatosis (histiocytosis X) and pulmonary precapillary hypertension. Pulmonary vascular resistances and mean pulmonary artery pressure decreased with corticosteroid therapy and dyspnea improved.

Publication types

Case Reports

MeSH terms

Adult
Blood Pressure / drug effects
Glucocorticoids / therapeutic use*
Histiocytosis, Langerhans-Cell / complications*
Histiocytosis, Langerhans-Cell / diagnostic imaging
Histiocytosis, Langerhans-Cell / pathology
Humans
Hypertension, Pulmonary / complications
Hypertension, Pulmonary / drug therapy*
Hypertension, Pulmonary / physiopathology
Lung / diagnostic imaging
Lung / pathology
Male
Prednisone / therapeutic use*
Pulmonary Circulation / drug effects
Radiography
Vascular Resistance / drug effects

Substances

Glucocorticoids
Prednisone