Review ArticlePathogenesis of malnutrition in cystic fibrosis, and its treatment
References (55)
- et al.
Growth patterns in children with cystic fibrosis
J Pediatr
(1964) - et al.
Perspectives in cystic fibrosis
Pediatr Clin North Am
(1979) - et al.
A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto
J Clin Epidemiol
(1988) Cystic fibrosis. A not-so-fatal disease
Pediatr Clin North Am
(1974)- et al.
and the Consensus Committee Nutritional assessment and management in cystic fibrosis: a consensus report
Am J Clin Nutr
(1992) - et al.
Colipase and lipase secretion in childhood-onset pancreatic insufficiency. Delineation of patients with steatorrhea secondary to relative colipase deficiency
Gastroenterology
(1984) - et al.
Gastroesophageal reflux in patients with cystic fibrosis
J Pediatr
(1985) - et al.
Energy expenditure of patients with cystic fibrosis
J Pediatr
(1987) - et al.
Increased energy expenditure in young children with cystic fibrosis
Lancet
(1988) - et al.
Gene/energy interaction in cystic fibrosis
Lancet
(1990)
The cystic fibrosis gene and resting energy expenditure
J Pediatr
(1991)
Protein turnover and resting energy expenditure in patients with undernutrition and chronic lung disease
Am J Clin Nutr
(1992)
Assessment of total energy expenditure in free-living patients with cystic fibrosis
J Pediatr
(1991)
Improved growth and clinical, nutritional, and respiratory changes in response to nutritional therapy in cystic fibrosis
J Pediatr
(1980)
Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis
J Pediatr
(1984)
Short-term clinical, nutritional, and functional effects of continuous elemental enteral alimentation in patients with cystic fibrosis
J Pediatr
(1984)
Chronic jejunostomy feeding with a non-elemental formula in undernourished patients with cystic fibrosis
Lancet
(1986)
Effects of long-term nutritional rehabilitation on body composition and clinical status in malnourished children and adolescents with cystic fibrosis
J Pediatr
(1985)
Nutritional rehabilitation in cystic fibrosis: controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease
Pediatr
(1986)
Relative underweight in cystic fibrosis and its prognostic value
Acta Paediatr Scand
(1978)
Longitudinal studies in cystic fibrosis
Therapy of cystic fibrosis of the pancreas
Pediatrics
(1960)
Energy intakes and low-fat diets in children with cystic fibrosis
J Pediatr Gastroenterol Nutr
(1983)
A rational approach to the nutritional care of patients with cystic fibrosis
J R Soc Med
(1989)
Nutritional management of cystic fibrosis
Ann Rev Nutr
(1993)
Gastrostomy Feeding
Extreme variability of response to enzyme therapy in patients with CF
Pediatr Pulmonol
(1997)
Cited by (124)
Low body mass index as a barrier to lung transplant in cystic fibrosis
2022, Journal of Cystic FibrosisEnteral tube feeding for individuals with cystic fibrosis: Cystic Fibrosis Foundation evidence-informed guidelines
2016, Journal of Cystic FibrosisDiagnosis and management of pancreatic exocrine insufficiency
2017, Medical Journal of AustraliaCitation Excerpt :A number of diseases and conditions are known to be associated with PEI. For example, PEI is estimated to occur in 94% of patients with chronic pancreatitis (10–15 years after clinical onset);10,11 > 85% of patients with cystic fibrosis;12-14 74% of patients after pancreatic resection surgery;15 and 92% of patients with unresectable pancreatic cancer.16 The general level of PEI prevalence (high to low probability) can be assigned to different patient populations (Box 2).9
BMI increase during early childhood in boys with cystic fibrosis and early adrenarche
2024, Pediatric Pulmonology
- f1
Correspondence to PBP, Division of Gastroenterology and Nutrition, The Hospital for Sick Children, 555 University Avenue, Toronto, Ontario, Canada M5G 1x8
Copyright © 2000 Harcourt Publishers Ltd. All rights reserved.