ReviewManagement of Primary Pulmonary Artery Sarcomas
Section snippets
Methods
A literature search of Ovid/Medline was performed using the terms “sarcoma,” “pulmonary artery,” “surgery,” and/or “chemotherapy,” and/or “radiation therapy.” The search was limited to English articles about humans in the past 17 years. Each article was screened for central primary PA sarcomas as the diagnosis for each patient. Patients with lung parenchymal disease were included as long as their primary tumor was a central primary PA sarcoma. The analysis only included PA sarcomas undergoing
Comment
Primary PA sarcomas are rare tumors, with fewer than 250 cases reported. Although surgical resection is the standard of care, radical complete resection is rarely reported for tumors involving the main PA, pulmonic valve, or right ventricular outflow tract. In patients undergoing PA resection instead of thrombectomy, in conjunction with chemotherapy, our series reports a long median survival of 71 months. This improved survival is thought to be due to two factors: aggressive resection with a
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