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The “Shrinking lung syndrome” in SLE, treatment with theophylline

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Summary

We report on a patient with systemic lupus erythematosus who developed a shrinking lung syndrome. The dyspnoea of the patient and the results of pulmonary function tests significantly improved during treatment with theophylline 750 mg daily. This is the first report of a successful treatment of the shrinking lung syndrome with theophylline.

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Van Veen, S., Peeters, A.J., Sterk, P.J. et al. The “Shrinking lung syndrome” in SLE, treatment with theophylline. Clin Rheumatol 12, 462–465 (1993). https://doi.org/10.1007/BF02231771

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