Demographics and descriptive statistics of the CF cohort
| Variable | n (%)/median (range) |
| Female sex | 24 (32%) |
| Pancreatic insufficiency | 67 (89%) |
| dF508/dF508, dF508/other, other/other | 38 (51%)/34 (45%)/3 (4%) |
| Age at diagnosis (years) | 0.8 (0.0–9.0) |
| Children treated with CFTR modulators | 1 (1%) |
| Children with CF-related diabetes mellitus | 2 (3%) |
| Chronically infected with Pa during study period | 22 (29%) |
| Age at onset of chronic Pa infection (years) | 13.0 (3.1–18.9) |
| Children with ABPA | 3 (4%) |
| Follow-up time* (years) | 9.0 (1.0–14.1) |
| Number of MBW examinations/child | 11 (1–18) |
| Number of chest CTs/child | 3 (1–5) |
| Chest CTs at MBW examinations (±3 days) | 146 (73%) |
*Time between the first and the last multiple breath washout or the last chest CT.
ABPA, allergic bronchopulmonary aspergillosis; CFTR, cystic fibrosis transmembrane conductance regulator; MBW, multiple breath washout; Pa, P. aeruginosa.