Table 1

Demographics and descriptive statistics of the CF cohort

Variablen (%)/median (range)
Female sex24 (32%)
Pancreatic insufficiency67 (89%)
dF508/dF508, dF508/other, other/other38 (51%)/34 (45%)/3 (4%)
Age at diagnosis (years)0.8 (0.0–9.0)
Children treated with CFTR modulators1 (1%)
Children with CF-related diabetes mellitus2 (3%)
Chronically infected with Pa during study period22 (29%)
Age at onset of chronic Pa infection (years)13.0 (3.1–18.9)
Children with ABPA3 (4%)
Follow-up time* (years)9.0 (1.0–14.1)
Number of MBW examinations/child11 (1–18)
Number of chest CTs/child3 (1–5)
Chest CTs at MBW examinations (±3 days)146 (73%)
  • *Time between the first and the last multiple breath washout or the last chest CT.

  • ABPA, allergic bronchopulmonary aspergillosis; CFTR, cystic fibrosis transmembrane conductance regulator; MBW, multiple breath washout; Pa, P. aeruginosa.