QOL-PCD scales mean scores and SDs for participant characteristics where we had hypothesised an association a priori
| Physical functioning | Social functioning | Vitality | Treatment burden | Upper respiratory symptoms | Lower respiratory symptoms | |
|---|---|---|---|---|---|---|
| Gender | ||||||
| Male (n=23) | – | 43.96 (32.74) | – | 69.61 (19.75) | – | 58.70 (15.32) |
| Female (n=49) | 35.37 (27.74) | 57.62 (24.37) | 43.20 (20.36) | |||
| p=0.284 | p=0.052 | p=0.004 | ||||
| Age | ||||||
| 18–22 years (n=26) | 88.21 (15.81) | – | 58.55 (20.50) | – | 46.47 (23.35) | 58.76 (16.72) |
| 23–36 years (n=21) | 69.21 (29.63) | 52.91 (20.20) | 43.25 (30.80) | 40.21 (19.63) | ||
| 37–55 years (n=15) | 56.88 (32.35) | 46.66 (20.30) | 42.22 (27.72) | 36.30 (19.90) | ||
| >55 years (n=10) | 49.33 (34.88) | 48.88 (23.54) | 55.00 (26.41) | 55.00 (24.21) | ||
| p<0.001 | p=0.355 | p=0.655 | p=0.001 | |||
| Pseudomonas | ||||||
| Yes (n=34) | 63.92 (33.43) | – | – | – | 43.63 (26.75) | 44.12 (20.51) |
| No (n=35) | 76.38 (26.78) | 48.57 (27.08) | 52.22 (21.86) | |||
| p=0.092 | p=0.448 | p=0.117 | ||||
| FEV1% predicted | ||||||
| <40 (n=11) | 41.82 (30.12) | – | – | – | 59.09 (24.28) | 44.44 (26.99) |
| ≥40 to <60 (n=14) | 63.81 (32.94) | 45.83 (26.90) | 42.86 (25.17) | |||
| ≥60 to <75 (n=16) | 77.33 (29.04) | 41.67 (28.87) | 48.88 (17.21) | |||
| ≥75 (n=29) | 80.46 (23.70) | 43.68 (26.51) | 51.92 (19.49) | |||
| p<0.02 | p=0.364 | p=0.563 | ||||
PCD, primary ciliary dyskinesia; QOL, quality of life.