Patient demographics and clinical characteristics at presentation
| IPF (n=110) | SSc (n=440) | Sarcoidosis (n=180) | |
|---|---|---|---|
| Mean (range) age, years | 64.6 (45–85) | 52.8 (15–83) | 39.6 (15–75) |
| Gender (F/M) | 31/79 | 356/84 | 93/87 |
| Median (range) FVC, % predicted | 69.3 (41–98.9) | 91 (40–158) | 96.9 (42.4–146.5) |
| Median (range) FEV1, % predicted | 74.2 (40–98.7) | 87 (29.2–136) | 91.9 (14.1–136) |
| Median (range) Tlco, % predicted | 40 (18.1–76.8) | 63 (20–124) | 75.1 (25.3–125.4) |
| Median (range) CPI | 52.8 (0.27–73.2) | 30.7 (−9.9–68.3) | 20.3 (−14.7–63.2) |
CPI, composite physiological index; FEV1, forced expiratory volume in 1 s; FVC, forced vital capacity; IPF, idiopathic pulmonary fibrosis; Tlco, lung carbon monoxide transfer factor.