Baseline characteristics of the Danish cystic fibrosis (CF) population
Birth cohort | |||||||
≥1948 | ≥1958 | ≥1968 | ≥1978 | ≥1988 | ≥1998 | Total | |
N (%) | 7 (1.5) | 42 (8.8) | 110 (23) | 105 (21.9) | 141 (29.4) | 74 (15.4) | 479 (100) |
Women | 1 (14.3) | 19 (45.2) | 48 (43.6) | 52 (49.5) | 74 (52.5) | 42 (56.8) | 236 (49.3) |
No. Delta F508 = 0 | 0 (0) | 0 (0) | 1 (0.9) | 4 (3.8) | 5 (3.5) | 5 (6.8) | 15 (3.1) |
No. Delta F508 = 1 | 2 (28.6) | 14 (33.3) | 26 (23.6) | 24 (22.9) | 42 (29.8) | 19 (25.7) | 127 (26.5) |
No. Delta F508 = 2 | 5 (71.4) | 28 (66.7) | 83 (75.5) | 77 (73.3) | 94 (66.7) | 50 (67.6) | 337 (70.4) |
Developed chronic Pseudomonas | 6 (85.7) | 31 (73.8) | 84 (76.4) | 55 (52.4) | 20 (14.2) | 5 (6.8) | 201 (42) |
Missing infection information | 0 (0) | 5 (11.9) | 2 (1.8) | 2 (1.9) | 1 (0.7) | 0 (0) | 10 (2.1) |
Pancreatic insufficient | 7 (100) | 42 (100) | 105 (95.5) | 99 (94.3) | 133 (94.3) | 73 (98.6) | 459 (95.8) |
Copenhagen | 7 (100) | 38 (90.5) | 83 (75.5) | 72 (68.6) | 79 (56) | 50 (67.6) | 329 (68.7) |
Alive | 4 (57.1) | 27 (64.3) | 79 (71.8) | 77 (73.3) | 132 (93.6) | 74 (100) | 393 (82) |
Developed CFRD | 3 (42.9) | 21 (50) | 41 (37.3) | 31 (29.5) | 22 (15.6) | 1 (1.4) | 119 (24.8) |
CFRD, cystic fibrosis related diabetes.