Table 1

Baseline characteristics of study participants

Study participants (n=19)
Age (years), mean±SD10.5±3.1
Pseudomonas aeruginosa +ve7
Body mass index, mean±SD17.0±3.0
Pancreatic insufficient, %84
ΔF508/ΔF508, %42
ΔF508 compound heterozygous %21
FVC % predicted, mean ± SD (range)101±11.3 (81–121)
FEV1 % predicted, mean ± SD (range)96±12 (80–118)
FEF25–75% predicted, mean ± SD (range)84±24 (53–120)
  • Pseudomonas aeruginosa +ve is defined as two or more positive cultures in the previous year and/or currently on inhaled antipseudomonal treatment.

  • % Predicted spirometry values were calculated using the equations of Weng et al.19

  • FEV1, forced expiratory volume in 1 s; FVC, forced vital capacity; FEF25–75, forced expiratory flow at 25–75% of the forced vital capacity.