Table 2

 Aetiology of cystic lung disease

Focal or multifocal cystic lung disease
    Congenital
        Bronchogenic cysts
        Pulmonary sequestration
        Congenital cystic adenomatoid malformations (CCAM)
    Infectious
        Pulmonary tuberculosis
        Coccidioidomycosis
        Pneumocystis carinii pneumonia
        Echinococcus granulosus or E multilocularis
    Lymphocytic interstitial pneumonia (LIP)
    Desquamative interstitial pneumonia (DIP)
Diffuse cystic lung disease
    Pulmonary Langerhans’ cell histiocytosis (PLCH)
    Lymphangioleiomyomatosis (LAM)
Honeycomb cystic lung disease
    Asbestosis
    Idiopathic pulmonary fibrosis
    Collagen vascular disease
    Hypersensitivity pneumonitis
    Sarcoidosis
Miscellaneous
    Cystic lung disease in Down’s syndrome118,119
    Birt-Hogg Dube syndrome120–122
    Trauma