Table 1

 Patient demographic and physiological data (17 patients)

Data are presented as mean (SD) or median (interquartile range).
FEV1, forced expiratory volume in 1 second; FVC, forced vital capacity; RV, residual volume; TLC, total lung capacity; Tlco, carbon monoxide transfer factor.
Age (years)57 (5.4)
Sex (F:M)4:13
Pack years39 (25–70)
Oral steroids10
Inhaled steroids17
Oxygen dependent10
Lung function (l, % predicted)
    FEV10.59 (0.20), 19 (6.3)
    FVC1.96 (0.63), 55 (15)
    RV5.53 (1.24), 250 (52)
    TLC7.90 (1.58), 136 (13)
    Tlco7.50 (2.40), 26 (9.0)
Arterial blood gases (on room air)
    Pao2 (kPa)9.2 (1.7)
    Paco2 (kPa)6.8 (1.3)
6 min walk distance (m)319 (266–373)