Sex/age | Chest radiographic stage | Associated treatment | Systolic PAP | ||
---|---|---|---|---|---|
Baseline | 3–6 months | Last evaluation | |||
Cyc, intravenous cyclophosphamide. | |||||
*Whatever the treatment at the time of PH diagnosis, each patient received at least high doses of oral prednisone (0.5–1 mg/kg). | |||||
†In these patients the measure obtained by Doppler echocardiography was confirmed by right heart catheterisation. | |||||
F/55 | 0 | Methotrexate | 66 | 35 | <30 mm Hg at 12 months |
M/61 | II | Oxygen, warfarin | 121 | 125† | Dead at 11 months |
F/52 | II | – | 60 | 40 | 30 mm Hg at 14 months |
M/28 | II | – | 77 | 60† | 30 mm Hg at 36 months |
M/63 | II | – | 80 | 82 | Dead at 18 months |
M/55 | IV | – | 50 | 55 | Not re-evaluated |
F/62 | IV | – | 45 | 45† | 50 mm Hg at 18 months† |
M/57 | IV | Oxygen | 80 | 85 | Transplanted at 14 months |
M/47 | IV | – | 83 | 100 | Transplanted at 39 months |
M/42 | IV | Oxygen, Cyc | 56 | 59 | 91 mm Hg at 48 months† |