Table 1

Characteristics of study subjects

Patients (n=18)Controls (n=9)
VC=vital capacity; FEV1=forced expiratory volume in 1 second.
M/F10/85/4
Mean (range) age (years)40 (23–57)27.5 (21–31)
Disease stage (I/II/III)6/9/3NA
Mean (SE) VC (% predicted)89.1 (3.5)95.5 (1.8)
Mean (SE) FEV1 % predicted81.6 (5.1)100.3 (2.7)