Bronchiectasis | ||||
---|---|---|---|---|
PCD (n=14) | Non-PCD | |||
Control (n=37) | Without CF (n=31) | With CF (n=20) | ||
PCD= primary ciliary dyskinesia; CF= cystic fibrosis; FEV1=forced expiratory volume in 1 second; FVC=forced vital capacity; IS=inhaled steroids; OS=oral steroids. | ||||
*p<0.05 v CF group; †p<0.05 v healthy control group. | ||||
Age (years) | 33 (2.8) | 35 (4.6)* | 45 (5.1)* | 25.7 (2.4) |
Sex (M/F) | 20/17 | 8/6 | 16/15 | 12/8 |
FEV1 (% predicted) | 94 (0.8) | 51 (5.1)† | 58 (6.1)† | 53 (5.9)† |
FVC (% predicted) | 99 (0.4) | 72 (4.2)† | 77 (3.1)† | 74 (3.3)† |
FEV1/FVC | 0.81 (0.001) | 0.62 (0.04)† | 0.65 (0.02)† | 0.62 (0.04)† |
Treatment | None | 7 IS | 19 IS; 2 OS | 8 IS |