Table 1

Mean (SD) demographic, anthropometric, and functional characteristics of study patients (n=12)

M/F8/4
Age (years)28 (6)
Height (cm)166 (8)
Weight (kg)53 (10)
FEV1 (% predicted)20 (5)
FVC (% predicted44 (9)
FEV1/FVC41 (10)
RV (% predicted)249 (69)
TLC (% predicted)104 (23)
pH7.38 (0.02)
Paco2 (kPa)7.1 (0.8)
Pao2 (kPa)7.6 (0.9)