Mean (SD) demographic, anthropometric, and functional characteristics of study patients (n=12)
| M/F | 8/4 |
| Age (years) | 28 (6) |
| Height (cm) | 166 (8) |
| Weight (kg) | 53 (10) |
| FEV1 (% predicted) | 20 (5) |
| FVC (% predicted | 44 (9) |
| FEV1/FVC | 41 (10) |
| RV (% predicted) | 249 (69) |
| TLC (% predicted) | 104 (23) |
| pH | 7.38 (0.02) |
| Paco2 (kPa) | 7.1 (0.8) |
| Pao2 (kPa) | 7.6 (0.9) |