Table 1

Patient characteristics

Men (n = 82) Women (n = 54)
Age (years)1-150 24.5 (20–31)24.0 (19–31)
Age at diagnosis (years)1-150 1.3 (<1–12.3)2 (<1–10)
FEV1(% predicted)1-150 52.6 (32.3–72.6)59.9 (44.5–75.5)
BMI (kg/m2)1-150 20.1 (18.5–22.6)21.0 (19.1–23.1)
Employed39 (48%)26 (48%)
Studying16 (20%)10 (19%)
Married/living with partner30 (37%)20 (37%)
One or more children1-151 5 (6%)14 (26%)
  • FEV1 = forced expiratory volume in one second; BMI = body mass index.

  • 1-150 Values are median (interquartile range).

  • 1-151 Five men with children four had successfully taken part in an assisted fertility programme.