Table 2

Details of pregnancies in patients with lymphangioleiomyomatosis (LAM)

Age when pregnantParity2-150Complications during pregnancyInterventions during pregnancyDelivery
LAM presenting in pregnancy:
27 1/1Bilateral pneumothoracesSurgical pleurectomy Caesarean section 32 weeks
32 1/1PneumothoraxIntercostal drainCaesarean section 38 weeks
28 2/2Bilateral chylous effusionsIntercostal drainNot specified
301/1Chylous effusionThoracotomy, thoracic duct ligation, OLB, pleurectomyUncomplicated
Pregnancies after LAM diagnosed2-160:
32 1/1PneumothoraxThoracotomy, OLB and pleurectomyCaesarean section 38 weeks
362/4NoneTermination at 12 weeks
291/1NoneNoneCaesarean section 38 weeks
  • OLB = open lung biopsy.

  • 2-150 Successful pregnancies/all pregnancies.

  • 2-160 LAM diagnosed at 108, 44, and 39 months before pregnancy, respectively.