Table 1

Mean (SD) demographic data of the study population

Index casesNon-index cases
No.27 (36%)48 (64%)
Deaths16 (59%) 5 (8.3%)
M/F12/1517/31
Age at diagnosis (years)56.2 (12.7)46.5 (13.9)
Follow up (years) 5.4 (3.9)10.6 (5.8)
α1-antitrypsin (μmol/l) 8.2 (3.0) 8.1 (2.8)