Table 1

Clinical data of patients with cystic fibrosis (CF)

CF patients (n = 89)CF children of parents questioned (n = 125)
MeanRangeSDMeanRangeSD
Shwachman score57.215–7512.761.820–7512.4
% of ideal body weight95.560–16614.895.672–1269.8
FEV1 1-150 55.616–11824.774.128–11822.5
Percentage of samplePercentage of sample
Pseudomonascolonisation66.344.0
Cirrhosis of the liver11.25.6
Insulin dependent diabetes14.60.8
  • 1-150 FEV1 was only obtained from children over the age of five which reduces the number of children in the parent sample from 125 to 95 for this variable.