TY - JOUR T1 - Pulmonary endarterectomy for calcified amorphous tumour-related pulmonary hypertension JF - Thorax JO - Thorax SP - 584 LP - 585 DO - 10.1136/thoraxjnl-2016-208939 VL - 72 IS - 6 AU - Peter I Bonta AU - Harm J Bogaard AU - Inge van den Berk AU - Hans W M Niessen AU - Allard van der Wal AU - Petr Symersky Y1 - 2017/06/01 UR - http://thorax.bmj.com/content/72/6/584.abstract N2 - A 42-year-old patient presenting with exertional dyspnoea was diagnosed with functional class II pulmonary hypertension (PH) with severe tricuspid valve insufficiency due to cardiac and pulmonary artery obstruction by calcified amorphous tumour (paCAT). Bilateral (sub)segmental perfusion defects were seen on ventilation/perfusion scan (see online supplementary figure S1), while the CT angiogram showed large amounts of calcified radio-opaque material in absence of radiological characteristics of chronic thromboembolic pulmonary hypertension (CTEPH), such as webs, stenosis or pouches (figure 1A, C). After multi-institutional (Amsterdam, NL and Papworth, Cambridge, UK) assessment of the case, a decision was made to perform a complete, bilateral, pulmonary endarterectomy (PEA) combined with tricuspid valve replacement. During PEA bone-hard material was retrieved that lacked the (sub)segmental pulmonary … ER -