TY - JOUR T1 - Familial primary spontaneous pneumothorax consistent with true autosomal dominant inheritance. JF - Thorax JO - Thorax SP - 151 LP - 152 DO - 10.1136/thx.53.2.151 VL - 53 IS - 2 AU - P J Morrison AU - R C Lowry AU - N C Nevin Y1 - 1998/02/01 UR - http://thorax.bmj.com/content/53/2/151.abstract N2 - A family exhibiting spontaneous pneumothorax in a father and three offspring (two sons, and one daughter) is described. The mode of inheritance is apparently autosomal dominant with two episodes of male to male transmission in one family. The age of onset varied by up to 13 years within the family. Isolated autosomal dominant pneumothorax appears to be a distinct clinical entity. ER -