RT Journal Article
SR Electronic
T1 Diagnosis of congenital cystic adenomatoid malformation of the lung in newborn infants and children.
JF Thorax
JO Thorax
FD BMJ Publishing Group Ltd and British Thoracic Society
SP 122
OP 125
DO 10.1136/thx.45.2.122
VO 45
IS 2
A1 H A Heij
A1 S Ekkelkamp
A1 A Vos
YR 1990
UL http://thorax.bmj.com/content/45/2/122.abstract
AB Seventeen patients were diagnosed as having congenital cystic adenomatoid malformation of the lung during 1970-88. One case was associated with congenital diaphragmatic hernia and the child died before operation. The other 16 children underwent successful surgery. The patients presented in one of three ways--with neonatal respiratory impairment (12 cases) requiring urgent diagnosis and treatment, with recurrent respiratory tract infections (3), and with pneumothorax (1). Diagnostic problems arose with the neonatal presentation. In four of the children laparotomy was performed for presumed diaphragmatic hernia; three of these children had right sided lesions. Congenital diaphragmatic hernia was excluded by contrast studies in a further two patients. Histological examination confirmed the diagnosis in all cases. The postoperative course was uneventful in all 16 patients. No long term impairment of pulmonary function was noted.