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Benign but fatal: management of endotracheal Rosai-Dorfman disease with acute onset
  1. Bin Wang1,
  2. Zhi-min Song2,
  3. Jin-dong Li1,
  4. Yin-long Zhao3,
  5. Ping-li Sun4,
  6. Jia-kun Tian5,
  7. Jin-zhi Yin6,
  8. Yan Zhang1
  1. 1Department of Thoracic Surgery, Jilin University Second Hospital, Changchun, Jilin, China
  2. 2Department of Anesthesiology, Jilin University Second Hospital, Changchun, Jilin, China
  3. 3Department of Radiology and Nuclear Medicine, Jilin University Second Hospital, Changchun, Jilin, China
  4. 4Department of Pathology, Jilin University Second Hospital, Changchun, Jilin, China
  5. 5Department of Intensive Care, Jilin University Second Hospital, Changchun, Jilin, China
  6. 6Department of Respiratory Medicine, Jilin University Second Hospital, Changchun, Jilin, China
  1. Correspondence to Dr Yan Zhang, Department of Thoracic Surgery, Jilin University Second Hospital, Changchun, Jilin 130041, China; zyan99{at}jlu.edu.cn

Abstract

Rosai-Dorfman disease (RDD) is a non-malignant condition mainly manifesting as a proliferation of histiocytes in lymph nodes. Endotracheal RDD (ERDD) with an acute onset presentation is extremely rare. There are few case reports of ERDD mainly concerning its pathology, diagnostics and bronchoscopic treatment, without providing sufficient clinical information from a comprehensive perspective. As a novel and challenging technique, tracheal resection and reconstruction (TRR) with spontaneous-ventilation video-assisted thoracoscopic surgery (SV-VATS) has been reported as feasible and safe in highly selected patients, but few centres have shared their experience with this approach. This case-based discussion includes not only practical issues in the management of a life-threatening ERDD patient, but also specialists’ views on the management of acute obstructive airway, and the surgeons’ reflection on TRR with SV-VATS.

  • Thoracic Surgery
  • Emergency Medicine
  • Bronchoscopy
  • Imaging/CT MRI etc
  • Critical Care

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Footnotes

  • Contributors YZ, J-dL and BW conceived and drafted the manuscript. The other authors acted as consultants in the clinical case described and edit end review the manuscript.

  • Funding This study was funded bt Natural Science Foundation of Jilin Province (20210101280JC).

  • Competing interests None declared.

  • Provenance and peer review Not commissioned; externally peer reviewed.