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Chest clinic
Case based discussion
Extrapulmonary lymphangioleiomyomatosis: a wolf in sheep's clothing
  1. Aurélie Maria Derweduwen1,
  2. Erik Verbeken2,
  3. Marguerite Stas3,
  4. Johny Verschakelen4,
  5. Johan Coolen4,
  6. Geert Verleden1,
  7. Wim Wuyts1
  1. 1Unit for Interstitial Lung Diseases, Department of Respiratory Medicine, University Hospital Leuven, Leuven, Belgium
  2. 2Department of Pathology, University Hospital Leuven, Leuven, Belgium
  3. 3Department of Oncological Surgery, University Hospital Leuven, Leuven, Belgium
  4. 4Department of Radiology, University Hospital Leuven, Leuven, Belgium
  1. Correspondence to Aurélie Maria Derweduwen, Unit for Interstitial Lung Diseases, Department of Respiratory Medicine, University Hospital Leuven, Herestraat 49, 3000 Leuven, Belgium; aurelie.derweduwen{at}uzleuven.be

Abstract

We present a case of a 32-year-old woman who was diagnosed with lymphangioleiomyomatosis (LAM) after detecting a mass in the upper anterior mediastinum. Two years after presentation another metastatic localisation of LAM occurred in the cervical region. With this article we would like to highlight the fact that there are still a lot of unanswered questions, especially regarding the best management of extrapulmonary LAM.

  • Extrapulmonary
  • lymphangioleiomyomatosis
  • mediastinum
  • management

https://doi.org/10.1136/thoraxjnl-2012-201973

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    Footnotes

    • Competing interests None.

    • Patient consent Obtained.

    • Provenance and peer review Not commissioned; externally peer reviewed.