Abstract

Two distinct pathological entities may be associated with the clinical picture of `primary pulmonary hypertension'. In the classical form the brunt of the pathology falls upon the pulmonary arteries with the characteristic development of dilatation lesions and necrotizing arteritis. In the second rarer type the pulmonary veins appear to be primarily involved. This paper describes the clinical and pathological features of such a case of `pulmonary veno-occlusive disease' occurring in a young girl.