Pathogenesis of cystic fibrosis

Lancet. 1993 Apr 24;341(8852):1065-9. doi: 10.1016/0140-6736(93)92422-p.
No abstract available

Publication types

  • Review

MeSH terms

  • Cystic Fibrosis / etiology*
  • Cystic Fibrosis / genetics
  • Cystic Fibrosis / physiopathology
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Humans
  • Ion Channels / genetics
  • Ion Channels / physiology
  • Membrane Proteins / genetics
  • Membrane Proteins / physiology
  • Pseudomonas Infections / microbiology
  • Pseudomonas Infections / physiopathology
  • Respiratory System / physiopathology
  • Respiratory Tract Infections / microbiology
  • Respiratory Tract Infections / physiopathology
  • Sweat Glands / physiopathology

Substances

  • CFTR protein, human
  • Ion Channels
  • Membrane Proteins
  • Cystic Fibrosis Transmembrane Conductance Regulator