No abstract available
MeSH terms
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Adenosine Triphosphate / pharmacology
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Adult
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Amiloride / pharmacology
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Bronchodilator Agents / pharmacology
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Chloride Channels / drug effects
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Chloride Channels / metabolism
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Chlorides / metabolism*
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Chlorides / pharmacology
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Cystic Fibrosis / genetics*
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Cystic Fibrosis / metabolism
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Cystic Fibrosis / physiopathology
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Cystic Fibrosis Transmembrane Conductance Regulator / genetics*
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Diuretics / pharmacology
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Female
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Forced Expiratory Volume / drug effects
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Forced Expiratory Volume / physiology
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Homozygote
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Humans
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Isoproterenol / pharmacology
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Male
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Membrane Potentials / drug effects
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Membrane Potentials / physiology
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Mutation / genetics*
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Retrospective Studies
Substances
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Bronchodilator Agents
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CFTR protein, human
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Chloride Channels
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Chlorides
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Diuretics
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Cystic Fibrosis Transmembrane Conductance Regulator
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Amiloride
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Adenosine Triphosphate
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Isoproterenol