Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion

Lancet. 1999 Mar 20;353(9157):984-5. doi: 10.1016/S0140-6736(98)05447-6.
No abstract available

Publication types

  • Letter

MeSH terms

  • Adenosine Triphosphate / pharmacology
  • Adult
  • Amiloride / pharmacology
  • Bronchodilator Agents / pharmacology
  • Chloride Channels / drug effects
  • Chloride Channels / metabolism
  • Chlorides / metabolism*
  • Chlorides / pharmacology
  • Cystic Fibrosis / genetics*
  • Cystic Fibrosis / metabolism
  • Cystic Fibrosis / physiopathology
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics*
  • Diuretics / pharmacology
  • Female
  • Forced Expiratory Volume / drug effects
  • Forced Expiratory Volume / physiology
  • Homozygote
  • Humans
  • Isoproterenol / pharmacology
  • Male
  • Membrane Potentials / drug effects
  • Membrane Potentials / physiology
  • Mutation / genetics*
  • Retrospective Studies

Substances

  • Bronchodilator Agents
  • CFTR protein, human
  • Chloride Channels
  • Chlorides
  • Diuretics
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Amiloride
  • Adenosine Triphosphate
  • Isoproterenol