Animal models of cystic fibrosis
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Keywords
Cystic fibrosis transmembrane conductance regulator
Genetics
Lung diseases
Microbiology
Pathology
Disease models
Animal
Intestines
Pathology
Mice
Genetics
Abbreviations
AML
amiloride
Bc
Burkholderia cepacia
BMT
bumetanide
Ca-ion
Ca2+-ionophore ionomycin
DIDS
4,4′-diisothiocyanatostilbene-2,2′-disulfonic acid
ENaC
epithelial sodium channel
FABP
fatty-acid-binding protein
FSK
forskolin
Hi
Haemophilus influenzae
iNOS
intracellular nitric oxide syntethase
KO
knockout
LPS
lipopolysaccharide
MCC
mucociliary clearance
Pa
Pseudomonas aeruginosa
PCL
periciliary liquid layer
RSV
respiratory syncytial virus
Sa
Staphylococcus aureus
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Copyright © 2004 European Cystic Fibrosis Society. Published by Elsevier B.V. All rights reserved.