Table 1

Baseline characteristics and haemodynamics of all patients in prevalence study

Aetiology/gendernAge (years)RAP (mm Hg)mPAP (mm Hg)CI (l/m2)PVR (dyne.cm-5)6MWD (m)NYHA II/III/IV
IPAH all8551.2 (16.7)*9.5 (5.4)52.0 (13.4)*2.0 (0.6)981 (462)*320 (117)*11/64/10
CTEPH all12060.3 (16.8)11.1 (6.3)46.8 (10.5)2.1 (0.6)801 (393)253 (117)9/83/28
IPAH premenopausal women2637.7 (7.9)9.2 (5.9)53.3 (12.0)*2.0 (0.6)986 (321)*342 (99)4/21/1*
CTEPH premenopausal women2638.0 (11.0)11.9 (6.0)45.0 (13.8)2.3 (0.7)752 (494)303 (126)4/14/8
IPAH postmenopausal women3464.5 (9.5)*9.8 (5.9)49.2 (12.5)2.0 (0.5)952 (464)278 (107)*1/26/7
CTEPH postmenopausal women4669.4 (9.3)9.5 (5.4)48.0 (10.2)2.1 (0.6)902 (427)202 (107)0/29/17
IPAH men2547.3 (18.1)*9.3 (3.9)54.5 (15.6)*2.0 (0.6)1014 (583)*343 (136)6/17/2
CTEPH men4863.9 (14.0)12.3 (7.0)46.6 (8.7)2.1 (0.5)729 (257)285 (104)5/40/3
  • * p<0.05 vs corresponding CTEPH group.

  • BMPR2, bone morphogenetic protein receptor type 2; CTEPH, chronic thromboembolic pulmonary hypertension; IPAH, idiopathic pulmonary arterial hypertension; mPAP, mean pulmonary artery pressure; PVR, pulmonary vascular resistance.