Diagnosis | Pre-MDT Diagnosis | Consensus diagnosis | 1 year transplant free survival | ||
n | % | n | % | % | |
Asbestosis | 10 | 1.5 | 11 | 1.7 | 81.8 |
CPFE | 26 | 4.0 | 33 | 5.1 | 78.8 |
CT-ILD | 79 | 12.1 | 68 | 10.4 | 98.5 |
Drug Related ILD | 16 | 2.5 | 14 | 2.2 | 92.9 |
Hypersensitivity pneumonitis | 63 | 9.7 | 71 | 10.9 | 85.9 |
IPF | 150 | 23.0 | 130 | 20.0 | 81.5 |
No ILD | 2 | 0.3 | 65 | 10.0 | 89.2 |
NSIP | 47 | 7.2 | 73 | 11.2 | 84.9 |
NSIP/UIP Spectrum | 12 | 1.8 | 6 | .9 | 83.3 |
Organising pneumonia | 11 | 1.7 | 11 | 1.7 | 90.9 |
Other (including vasculitis, DIP, LAM etc) | 33 | 5.1 | 30 | 4.6 | 90 |
Pulmonary Langerhans Cell Histiocytosis | 5 | 0.8 | 7 | 1.1 | 100 |
RB-ILD | 10 | 1.5 | 13 | 2.0 | 100 |
Sarcoidosis | 84 | 12.9 | 74 | 11.4 | 97.3 |
Unclassifiable ILD | 103 | 15.8 | 45 | 6.9 | 84.3 |
Total | 651 | 100.0 | 651 | 100.0 | 88.2 |
CPFE: Combined Pulmonary Fibrosis/Emphysema, CT-ILD: Connective Tissue disease-associated ILD, IPF: Idiopathic Pulmonary Fibrosis, NSIP: Non-specific Interstitial Pneumonia, UIP: Usual Interstitial Pneumonia, RB-ILD: Respiratory Bronchiolitis-ILD, DIP: Desquamative Interstitial Pneumonia, LAM: Lymphangioleiomyomatosis