Case Number | Diagnosis | Immunosuppression Regimen | Age | Onset of symptoms to ECMO initiation (days) | CT DAD (%) | CT Total Abnormality (%) | SOFA Score | CRP |
1 | Eosinophilic pneumonia; Hypereosinophilic syndrome | IVMP | 30 | 21 | 100 | 82.5 | 7 | 344 |
3 | Eosinophilic pneumonia | IVMP | 26 | 12 | 0 | 80.0 | 9 | 285 |
10 | Organising pneumonia | IVMP + CYC | 52 | 30 | 10 | 66.8 | 12 | 226 |
11 | Acute interstitial pneumonitis | IVMP + RTX | 44 | 17 | 100 | 88.8 | 11 | 497 |
12 | Anti-Jo 1 associated acute interstitial pneumonitis | IVMP + CYC + RTX | 42 | 25 | 10 | 82.1 | 11 | 350 |
13 | DD: AIP, eosinophilic pneumonia, Organising pneumonia | IVMP | 35 | 19 | 90 | 91.7 | 13 | 266 |
Mean | 38.2 | 20.7 | 51.7 | 82.0 | 10.5 | 328 | ||
NON-RESPONDERS | ||||||||
2 | Acute interstitial pneumonitis | IVMP + CYC | 54 | 129 | 88.4 | 68.4 | 6 | 70 |
4 | Idiopathic pleuropulmonary fibroelastosis | None | 45 | 140 | 81.3 | 81.2 | 7 | 117 |
5 | Acute Interstitial pneumonitis; Organising pneumonia | IVMP + CYC + RTX plus heart lung transplant | 46 | 26 | 50 | 85.9 | 9 | 153 |
6 | Unclassifiable | IVMP + CYC + RTX | 20 | 46 | 100 | 96.7 | 7 | 66 |
7 | Bleomycin-induced fibrosis | IVMP | 46 | 29 | 82.5 | 85.8 | 9 | 111 |
8 | Clinically amyopathic Dermatomyositis with acute interstitial pneumonitis | IVMP + RTX | 29 | 172 | 100 | 95.6 | 4 | 71 |
Mean | 40 | 90.3 | 83.7 | 85.6 | 7.0 | 98 | ||
P-values | 0.79 | 0.04 | 0.19 | 0.53 | 0.01 | 0.046 |
Key: IVMP: Intravenous Methylprednisolone, RTX: Rituximab, CYC: Cyclophosphamide