TableĀ 1

Reported cases of isolated unilateral pulmonary vein atresia in adults

ReferenceSymptomsAge at diagnosisGenderSide affectedSurgery
Harrison et al1Haemoptysis, haematemesis27FLPneumonectomy
Heyneman et al2Dyspnoea, pulmonary artery hypertension25FRPneumonectomy
Heyneman et al2Dyspnoea, haemoptysis43FRPneumonectomy
Zhang et al3Haemoptysis22FRPneumonectomy
SavasBosbas et al4Dyspnoea20FRConservative
Current patientHaemoptysis33MRAttempted pneumonectomy