Table 1

Baseline characteristics of the Danish cystic fibrosis (CF) population

Birth cohort
≥1948≥1958≥1968≥1978≥1988≥1998Total
N (%)7 (1.5)42 (8.8)110 (23)105 (21.9)141 (29.4)74 (15.4)479 (100)
Women1 (14.3)19 (45.2)48 (43.6)52 (49.5)74 (52.5)42 (56.8)236 (49.3)
No. Delta F508 = 00 (0)0 (0)1 (0.9)4 (3.8)5 (3.5)5 (6.8)15 (3.1)
No. Delta F508 = 12 (28.6)14 (33.3)26 (23.6)24 (22.9)42 (29.8)19 (25.7)127 (26.5)
No. Delta F508 = 25 (71.4)28 (66.7)83 (75.5)77 (73.3)94 (66.7)50 (67.6)337 (70.4)
Developed chronic Pseudomonas 6 (85.7)31 (73.8)84 (76.4)55 (52.4)20 (14.2)5 (6.8)201 (42)
Missing infection information0 (0)5 (11.9)2 (1.8)2 (1.9)1 (0.7)0 (0)10 (2.1)
Pancreatic insufficient7 (100)42 (100)105 (95.5)99 (94.3)133 (94.3)73 (98.6)459 (95.8)
Copenhagen7 (100)38 (90.5)83 (75.5)72 (68.6)79 (56)50 (67.6)329 (68.7)
Alive4 (57.1)27 (64.3)79 (71.8)77 (73.3)132 (93.6)74 (100)393 (82)
Developed CFRD3 (42.9)21 (50)41 (37.3)31 (29.5)22 (15.6)1 (1.4)119 (24.8)
  • CFRD, cystic fibrosis related diabetes.