CF | Ctrl | HIRT | HIRT-Nl | HIRT-CF | HIRT/Ctrl | HIRT/CF | HIRT-Nl/Ctrl | HIRT-Nl/CF | HIRT-CF/Ctrl | HIRT-CF/CF | HIRT-Nl/HIRT-CF | |
No. of patients | 67 | 29 | 21 | 8 | 13 | p Value | p Value | p Value | p Value | p Value | p Value | p Value |
Age (years) | 14 (7.5) | 27 (11) | 2 (2.1) | 1.7 (2.9) | 2 (1.8) | <10−4 | <10−4 | <10−4 | <10−4 | <10−4 | <10−4 | 0.71 |
Maximum basal PD | −51 (16) | −15 (11) | −22.5 (14) | −17 (12) | −30 (15) | 0.003 | <10−4 | 0.42 | <10−4 | <10−4 | <10−4 | 0.02 |
ΔAmiloride | 28 (17) | 6 (6.7) | 9 (6.7) | 6.3 (3.5) | 12.2 (7) | 0.03 | <10−4 | 0.74 | <10−4 | 0.01 | <10−4 | 0.004 |
∆LowCl–-Iso | 0 (7) | −15 (11) | −6 (5.7) | −9 (4) | −3 (4) | <10−4 | <10−4 | 0.008 | <10−4 | <10−4 | 0.0006 | 0.0006 |
Results are presented as median (IQR). Comparison with Mann–Whitney test.
Patients with HIRT-Nl have a diagnostic score >0.27, patients with HIRT-CF have a diagnostic score ≤0.27.