Idiopathic pulmonary fibrosis (IPF)* | 68% |
Other forms of interstitial lung disease | 32% |
Sarcoidosis | 10% |
Pulmonary lymphangiomyomatosis | 4% |
Connective tissue diseases | 2% |
Histiocytosis X | 1% |
Other† | 15% |
Interstitial lung disease is the diagnosis in 25% of all lung transplantations.
*Recorded in the Registry as IPF, not as histological subtype. However, a large majority will be the usual interstitial pneumonia (UIP) form of idiopathic interstitial pneumonia.
†Not specified but including occupational lung diseases; chemotherapy/radiotherapy related; extrinsic allergic alveolitis.