Table 1

Baseline data

Case 1Case 2Case 3Case 4
Age on presentation (years)27464435
Smoking history
 Tobacco15 pack years7 pack years3 pack years2–5 cigars per day
 MarijuanaSeveral pipes per day2–3 joints per day2–3 joints per day2 joints per week
Alpha1-antitrypsin (g/l) (NR 1.1–2.1)2.11.51.92.6
FVC (l) (% predicted)5.1 (106)4.6 (103)2.7 (72)2.9 (59)
FEV1 (l) (% predicted)3.9 (97)3.3 (100)2.5 (78)1.8 (44)
FEV1/FVC (%)77729462
Tlco mmol/kPa/min (% predicted)9.9 (96)5.9 (46)7.3 (72)3.9 (35)
Kco mmol/kPa/min/l (% predicted)1.7 (89)1.4 (58)1.6 (78)1.0 (49)