Demographic and clinical details of familial CFA cases
| Mean (SE) age | 58 (2.5) years |
| Mean (SE) age at diagnosis | 55 (2.5) years |
| Male:female ratio | 1.75:11-150 |
| Percentage ever smokers | 52% |
| Median pack years | 28.3 (range 2–75) |
| Symptoms and signs | |
| Breathlessness | 94% |
| Cough | 86% |
| Chest pain | 18% |
| Clubbing | 53% |
| Basal crepitations | 88% |
↵1-150 p<0.05 (χ2 test).