Table 3

Congenital cystic adenomatoid malformation

CharacteristicsType 1Type 2Type 3
Frequency6.5%2.5%10%
Associated anomalies8%56%Nil
Cyst size (cm)3–10 0.5–3<0.5
Predominant epitheliumCiliated pseudostratified columnarCiliated columnar and cuboidalCuboidal (minimal ciliation)
Mucous cells32%NilNil
Cartilage10%NilNil
Striated muscleNil12%Nil
Presence of intervening pulmonary parenchymaYesYesNo
PrognosisGoodGoodPoor