Clinical features of 21 patients with pulmonary lymphangioleiomyomatosis
| Case1-150 | Age at onset1-151 | Sex | Initial manifestations | Later manifestations | Tuberous sclerosis | Associated conditions |
|---|---|---|---|---|---|---|
| 19 | 34 | F | Dyspnoea | Cough, haemoptysis | No | Mimic tuberculosis1-152 |
| 210 | 40 | F | Pneumothorax (6)1-153 | None | No | Uterine myoma |
| 310 | 48 | F | Pneumothorax (1) | Chest pain, dyspnoea | No | None |
| 410 | 20 | F | Dyspnoea | Haemoptysis, pneumothorax (4) | Yes | None |
| 510 | 32 | F | Pneumothorax (1) | Cough, chest pain, dyspnoea | No | Active tuberculosis1-155 |
| 6 | 35 | F | Dyspnoea | Haemoptysis | No | None |
| 7 | 26 | F | Pneumothorax (3) | Dyspnoea | No | Pregnancy |
| 8 | 22 | F | Dyspnoea | Pneumothorax (4) | Yes | Transplantation1-154 |
| 9 | (55) | F | Dyspnoea | Cough | No | None |
| 10 | 42 | F | Dyspnoea | None | No | None |
| 1111 | 29 | F | Dyspnoea | None | No | None |
| 1212 | 38 | F | Pneumothorax (2) | Chest pain, dyspnoea | Yes | None |
| 1313 | 20 | F | Pneumothorax (1) | Chest pain, dyspnoea | No | None |
| 1414 | 27 | F | Dyspnoea | None | Yes | Mimic tuberculosis1-152 |
| 1515 | 29 | F | Dyspnoea | Haemoptysis | No | Clomiphene therapy |
| 1616 | 47 | F | Dyspnoea | Cough, pneumothorax (1) | No | None |
| 1717 | 26 | F | Pneumothorax (3) | Chest pain, dyspnoea | No | Pregnancy |
| 1818 | 37 | F | Pneumothorax (3) | Chest pain, dyspnoea | Yes | None |
| 1919 | 26 | F | Pneumothorax (5) | None | No | Pregnancy |
| 2020 | (34) | F | Dyspnoea | None | No | None |
| 2121 | 23 | F | Pneumothorax (2) | Dyspnoea | Yes | None |
↵1-150 Superscript numbers following case numbers refer to references.
↵1-151 Age at onset means the age at the onset of symptoms, but where the age is in parentheses this is the age on her first visit to the physician.
↵1-152 They were erroneously diagnosed as miliary tuberculosis at first.
↵1-153 Number in parentheses following pneumothorax indicates frequency of pneumothorax.
↵1-155 She had concurrent pulmonary tuberculosis and was given anti-tuberculous medications.
↵1-154 She underwent bilateral sequential lung transplantation.