Lymphomatoid granulomatosis mimicking interstitial lung disease

Respirology. 2008 Nov;13(7):1085-7. doi: 10.1111/j.1440-1843.2008.01351.x. Epub 2008 Aug 10.

Abstract

Lymphoid granulomatosis is a rare form of pulmonary angiitis. This case report presents a patient with lymphoid granulomatosis in whom the clinical presentation, radiological features and the partial response to corticosteroid therapy mimicked interstitial lung disease. Lymphoid granulomatosis was only diagnosed at post-mortem examination. The range of reported clinical presentations, diagnostic approaches and outcomes are described.

Publication types

  • Case Reports

MeSH terms

  • Antigens, CD20 / immunology
  • Biopsy
  • Bronchoalveolar Lavage
  • Bronchoalveolar Lavage Fluid / cytology
  • Bronchoscopy
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Follow-Up Studies
  • Humans
  • Immunohistochemistry
  • Lung Diseases, Interstitial / diagnosis*
  • Lung Neoplasms / diagnosis*
  • Lung Neoplasms / metabolism
  • Lymphocytes / immunology
  • Lymphocytes / pathology
  • Lymphomatoid Granulomatosis / diagnosis*
  • Lymphomatoid Granulomatosis / metabolism
  • Middle Aged
  • Oncogene Proteins, Viral
  • Tomography, X-Ray Computed
  • Viral Matrix Proteins / metabolism

Substances

  • Antigens, CD20
  • EBV-associated membrane antigen, Epstein-Barr virus
  • Oncogene Proteins, Viral
  • Viral Matrix Proteins