Hereditary haemorrhagic telangiectasia and pulmonary arteriovenous malformations: issues in clinical management and review of pathogenic mechanisms

Thorax. 1999 Aug;54(8):714-29. doi: 10.1136/thx.54.8.714.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Antigens, CD
  • Arteriovenous Malformations / pathology*
  • Embolization, Therapeutic / methods
  • Endoglin
  • Genotype
  • Humans
  • Mutation / genetics
  • Phenotype
  • Protein Serine-Threonine Kinases*
  • Pulmonary Artery / abnormalities*
  • Pulmonary Veins / abnormalities*
  • Receptors, Cell Surface
  • Receptors, Growth Factor / metabolism
  • Receptors, Transforming Growth Factor beta*
  • Telangiectasia, Hereditary Hemorrhagic / pathology
  • Telangiectasia, Hereditary Hemorrhagic / therapy*
  • Tomography, X-Ray Computed
  • Transforming Growth Factor beta / metabolism
  • Vascular Cell Adhesion Molecule-1 / genetics

Substances

  • Antigens, CD
  • ENG protein, human
  • Endoglin
  • Receptors, Cell Surface
  • Receptors, Growth Factor
  • Receptors, Transforming Growth Factor beta
  • Transforming Growth Factor beta
  • Vascular Cell Adhesion Molecule-1
  • Protein Serine-Threonine Kinases