Mitral stenosis obscuring the diagnosis of plexogenic pulmonary arteriopathy and familial pulmonary hypertension
- David Langlebena,
- Esther Lamoureuxa,
- Francois Marcottea,
- Robert Schlesingera,
- Leonidas Dragatakisa,
- Marie Josee Crowea,
- Yves Langloisa,
- Francois Lemirec,
- Michel Whiteb
- aDepartments of Cardiology, Pathology, Cardiovascular Surgery, and Intensive Care, Sir Mortimer B. Davis Jewish General Hospital, McGill University, Montreal, Quebec, Canada, bDepartment of Cardiology, Institut de Cardiologie de Montreal, Montreal, Quebec, Canada, cHotel Dieu de Montreal, University of Montreal, Montreal, Quebec, Canada
- Dr D Langleben, Jewish General Hospital, 3755 Cote Ste Catherine, Montreal, Canada H3T 1E2
- Received 22 December 1997
- Revision requested 16 March 1998
- Revised 15 May 1998
- Accepted 9 July 1998
Abstract
A patient who died after surgery for critical mitral stenosis was found to have underlying unrecognised plexogenic pulmonary arteriopathy and familial pulmonary hypertension. The importance of recognising familial pulmonary hypertension is discussed, together with the contribution of genetic and other risk factors to plexogenic pulmonary arteriopathy.
- plexogenic pulmonary arteriopathy
- mitral stenosis
- familial pulmonary hypertension
- primary pulmonary hypertension
Footnotes
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Funding: Dr Langleben is a Chercheur-Boursier Clinicien (Research Scholar) of the Fonds de la Recherche en Sante du Quebec.
