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Thorax 55:143-146 doi:10.1136/thorax.55.2.143
  • Original article

Adult familial cryptogenic fibrosing alveolitis in the United Kingdom

Table 1

Demographic and clinical details of familial CFA cases

Mean (SE) age 58 (2.5) years
Mean (SE) age at diagnosis 55 (2.5) years
Male:female ratio 1.75:11-150
Percentage ever smokers 52%
Median pack years 28.3 (range 2–75)
Symptoms and signs
 Breathlessness 94%
 Cough 86%
 Chest pain 18%
 Clubbing 53%
 Basal crepitations 88%
  • 1-150 p<0.05 (χ2 test).

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